Oral Pathology
Muneeb Shaikh, DDS
Pediatric Dentistry Resident
Indiana University, Bloomington, IN
INDIANA UNIVERSITY SCHOOL OF DENTISTRY, RILEY HOSPITAL FOR CHILDREN
Indianapolis, Indiana, United States
Jeffrey A. Dean, DDS MSD
Professor
Riley Hospital for Children
Indianapolis, Indiana, United States
LaQuia A. Vinson, DDS, MPH
Pediatric Dentistry Residency Program Director
Indiana University/Riley Hospital for Children
Indianapolis, Indiana, United States
Jeffrey A. Dean, DDS MSD
Professor
Riley Hospital for Children
Indianapolis, Indiana, United States
Dental management of a case of severe epidermolysis bullosa in a pediatric patient.
Muneeb Shaikh DDS · Jeffrey Dean DDS, MSD
(Indiana University Riley Hospital for Children, Indianapolis, IN)
Introduction:
Epidermolysis bullosa (EB) is a rare genetic skin disorder categorized by blistering due to mechanical trauma. This disorder presents in 4 different types: dystrophic EB, EB simplex, junctional EB and Kindler Syndrome. The fragile blistering skin occurs on extra-oral tissue, but in extreme cases, may occur on internal mucosal tissues such as the mouth and the lining of the stomach. Common oral findings of the disease include microstomia, intraoral ulcerations and bullae formation, ankyloglossia, tongue atrophy, elimination of buccal and vestibular sulci, lingual depapillation and atrophy of the palatal folds1.
Case Abstract:
A 7 year old female patient with medical history significant for epidermolysis bullosa presents to Riley ED for influenza A and adenovirus. Patient has been followed by a pediatric dentist and parent was concerned that ulcers were secondary to infection of dental origin. Patient’s symptoms include bilateral mouth and cheek pain as well purulent discharge occurring more than 1 month. Clinical exam revealed multiple ulcers on extraoral and intraoral tissues. The lesions were painful and oral tissues were very friable. This case study will explore the dental management of epidermolysis bullosa.