Syndromes/Craniofacial Anomalies
Emily N. Steiner, DMD (she/her/hers)
Pediatric Dental Resident
Case Western Reserve University — UH Rainbow Babies and Children’s Hospital, Cleveland, OH
CLEVELAND HEIGHTS, Ohio, United States
Margaret Elaine Ferretti, DMD, MPH
Program Director
Case Western Reserve University
Rainbow Babies and Children's Hospitals, Case Western Reserve University
Cleveland, Ohio, United States
Gerald A. Ferretti, DDS, MS, MPH
Professor and Chair
Case Western Reserve University
Cleveland, Ohio, United States
Regional odontodyspiasia (RO) is a rare, non-hereditary, developmental dental anomaly of unknown etiology that can affect both the deciduous and permanent dentition. RO is diagnosed based on clinical, radiographic and/or histopathologic findings consistent with severe hypoplasia and hypomineralization of both the enamel and dentin. RO most commonly occurs in the maxilla with a greater predilection for anterior vs. posterior teeth, generally unilateral in nature, rarely crosses the midline and rarely involves more than a single quadrant. Theories pertaining to the underlying pathophysiology include local trauma, local circulatory disorders, infection, teratogenic drugs, and neural crest cell defects. This poster will review present a case of regional odontodysplasia with three unusual features: 1. Involvement of two quadrants 2. Location in the mandible and 3. Presence of normal-appearing teeth among the dysplastic teeth.