A Case Report on Dental Management of a Pediatric Patient With Pierre Robin Sequence

Introduction: Pierre Robin sequence (PRS) is a syndrome defined by micrognathia, glossoptosis, and upper airway compromised with or without cleft palate. Etiology is still unclear, but 30% of PRS patients have associated genetic syndromes, most commonly Stickler syndrome and velocardiofacial syndrome.

Case report: This presentation discusses a 13 year old female who as Pierre robin sequence as well as Stickler syndrome. The patient had bilateral mandibular distraction osteogenesis when she was 22-day-old. When the patient turned 5, hypoplastic mandibular primary and permanent 1^st molars were noted. When the patient was 7, odontoma was noted coronal to #30. When the patient was 9, early extractions of mandibular permanent 1^st molars were rendered. This report will include clinical and dental findings associated with Pierre robin sequence, complications of distraction osteogenesis including odontoma, successful early extractions of permanent 1^st molars before eruption of permanent 2^nd molars, and overall dental management.